Cerebellar α-Ketoglutarate dehydrogenase activity is reduced in spinocerebellar ataxia type 1
Brain α-Ketoglutarate Dehydrotenase Complex Activity in Alzheimer's Disease
Immunoreactive Levels of α-ketoglutarate Dehydrogenase Subunits in Friedreich's Ataxia and Spinocerebellar Ataxia Type 1